RAMSEY HUNT Syndrome and Neuromuscular Retraining (EMG)
ESSENTIAL ELEMENTS FOR EFFECTIVE NEUROMUSCULAR RETRAINING
taken from: http://www.bellspalsy.ws
Proper Treatment Environment
A quiet, individual room where therapy is conducted without distractions, establishes the proper learning environment. Anyone who has worked with facial paralysis patients is aware of the social stigma associated with this disability. Privacy is essential to create a "safe" environment for the patient who is embarrassed by his or her appearance. In this setting, psychosocial issues can also be discussed.
Sensory Feedback
Optimal learning depends on making maximal use of sensory information. Accurate, proportional and immediate sensory feedback provides the information required for modification and learning of new motor patterns. Visual (mirror) feedback is the most commonly used type of feedback in the clinic and at home. Inexpensive and portable, mirrors provide the patient with immediate feedback regarding performance. Proprioception provides internal facial position sense and is essential for accurate exercise practice and generalization of movements outside of the clinical setting.
Surface EMG Feedback
Just as intraoperative EMG facial nerve monitoring has led to modifications in surgical techniques by providing the surgeon with specific feedback, sEMG monitoring of facial muscles during NMR can lead to modification of facial movement patterns by providing the patient with feedback regarding motor performance. It is an important tool in neuromuscular retraining of facial paralysis.
Also referred to as EMG biofeedback or EMG rehabilitation (EMGR), its purpose is "to bring the normally unconscious control of specific muscles under conscious control". Surface EMG feedback provides the patient with immediate information regarding the rate and strength of the muscle contraction in real time. As part of a neuromuscular retraining program sEMG feedback is used as an evaluative, as well as therapeutic tool to:
- Increase activity in weak muscles
- Decrease activity in hyperactive muscles and
- Improve coordination of muscle groups.
Surface electrodes placed on the skin over the muscle(s) being monitored detect electrical activity produced by the muscle contraction. The amplified signals are displayed on a video monitor. Patients observe this feedback and vary the manner in which they produce a specific movement until the desired pattern is achieved. By correlating information from sEMG feedback with mirror and proprioceptive feedback, the patient learns to reproduce the new movement patterns outside of the clinical setting and within the context of the home exercise program.
Other considerations of conditions similar to
Bell's Palsy
RAMSEY HUNT SYNDROME
Ramsey Hunt syndrome is similar to Bell's palsy. Unlike Bells palsy, the virus that causes Ramsey-Hunt syndrome has been conclusively identified. It is varicella zoster virus (VZV), which is the virus that causes chicken pox, and is a strain of the Herpes virus. Like HSV-1, it remains in the body, residing on nerve tissue in a dormant state on nerve ganglia after the initial infectious stage has passed. VZV typically remains dormant for decades. The incidence of Ramsey Hunt syndrome increases significantly after age 50. Younger patients with Ramsey-Hunt syndrome are often advised to be tested for autoimmune deficiencies.
Ramsey-Hunt syndrome results in symptoms that are in many respects identical to Bell's palsy. The symptoms are so alike that a diagnosis of Ramsey Hunt syndrome can easily be missed.
When the VSV virus is reactivated the resulting eruptions (blisters) are known as shingles. The first symptom is usually severe pain. There may also be a fever, headache, and localized tenderness. Blisters typically begin to emerge 1.5 to 3 days after the onset of these symptoms, although they may emerge with no prior symptoms.
Symptoms of Ramsey Hunt Syndrome
In addition to the "classic" symptoms of Bells palsy, Ramsey Hunt syndrome is associated with some additional symptoms that help differentiate it. Knowledge of these symptoms is key to an early diagnosis, and should be brought to a doctor's attention during the first visit, or when any of these symptoms become apparent.
1. Pain: Bell's palsy patients may complain of pain (often in or behind the ear) which can be acute. However, it will tend to fade within a week or two. The pain associated with Ramsey Hunt syndrome is often more severe, and more likely to be felt inside the ear. It may start before muscle weakness is apparent, and may last for weeks or months - sometimes longer. Medications such as Neurontin can ease the post-herpatic pain of Ramsey Hunt syndrome.
2. Vertigo: Dizziness is occasionally reported by Bells palsy patients, but is often associated with Ramsey Hunt syndrome. It can be more severe, and longer lasting.
3. Hearing loss: Unlike Bell's palsy, Ramsey Hunt syndrome can also affect the auditory nerve (CN-VIII), resulting in hearing deficit. This should not occur with Bells palsy, and is an important clue to the diagnosing physician. In some cases hearing loss will continue after facial muscle function returns.
4. Blisters: The primary symptom that makes a diagnosis of Ramsey Hunt syndrome likely is the appearance of blisters (known as shingles, or herpes zoster) in the ear. The blisters can appear prior to, concurrent to, or after the onset of facial paralysis. They can be expected to last 2 - 5 weeks, and can be quite painful. The pain can continue after the blisters have disappeared. Blisters are often the only clearly visible symptom that identifies Ramsay Hunt. Unfortunately, they may not be evident during the diagnostic examination. They can be present, but too deep within the ear to be visible. Or they can be too small to be seen. In some cases they may not appear until a week or more after the onset of muscle weakness. At times they do not appear in the ear at all, but may be present in the mouth or throat. It is also possible for the virus to reactivate without blisters at all.
5. Swollen and tender lymph nodes near the affected area.
While Bell's palsy is not contagious, shingles blisters are infectious. Contact with an open blister by someone who has never had chickenpox can result in transmission of the virus. The result will be chickenpox, not shingles or facial paralysis.